| CASE REPORT |
|
| Year : 2017 | Volume
: 6
| Issue : 1 | Page : 95 |
|
|
Hirayama's Disease: A Rare Clinical Variant of Amyotrophic Lateral Sclerosis
Swati C Aundhakar, Sanket K Mahajan, Daanish A Chhapra
Department of Medicine, Krishna Institute of Medical Sciences University, Karad, Maharashtra, India
Correspondence Address:
Swati C Aundhakar
Saurabh Hospital 140, Budhwar Peth, Karad - 415 110, Maharashtra
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/2277-9175.211797
|
|
|
Hirayama's disease is a rare clinical variant of amyotrophic lateral sclerosis where distal muscles are involved more compared to proximal muscles and vice-versa occurs only in 10% cases and so it is differentiated from O'Sullivan McLeod syndrome which involves only small muscles of single limb. Here, we present a case of Hirayama's disease where disease achieved a plateau after 3 years with no further progression. His electrophysiological studies, and clinical picture, and magnetic resonance imaging findings were consistent with a diagnosis of Hirayama's disease. |
|
|
|
| [FULL TEXT] [PDF]* |
|
 |
|
